Streeter Syndrome, also known as Amniotic Band Syndrome or Amniotic Constriction Bands, is a rare congenital disorder primarily characterized by the presence of fibrous bands or strands that adhere to and restrict fetal development within the uterus during pregnancy. The condition is caused when the inner amniotic lining ruptures or tears, leading to the formation of thin strands that wrap around or entangle various parts of the developing fetus.
Streeter Syndrome typically manifests in a wide range of abnormalities, affecting the limbs, fingers, toes, craniofacial region, and internal organs of the affected individual. The severity and extent of the deformities can vary significantly from case to case, leading to unique presentations and challenges for each person affected by the syndrome. Signs and symptoms may include malformed limbs or digits, syndactyly (fusion of fingers or toes), clubfoot, cleft lip or palate, facial asymmetry, and other structural malformations.
Diagnosis of Streeter Syndrome usually occurs prenatally through detailed ultrasound examinations that detect the presence of fibrous bands and associated abnormalities. However, in some cases, diagnosis may only occur after birth when physical anomalies become apparent. Surgical intervention may be recommended to release the constricting bands and correct limb or organ abnormalities if medically necessary.
Currently, there is no known cure for Streeter Syndrome. Treatment primarily focuses on managing and correcting the physical abnormalities through surgical techniques, orthotics, prosthetics, and rehabilitation programs to improve function and quality of life for individuals living with the condition. Additionally, genetic counseling may be offered to affected families to discuss the likelihood of recurrence in future pregnancies.
