Steely Hair Syndrome, also known as Uncombable Hair Syndrome (UHS), is a rare genetic disorder characterized by abnormal hair growth and structure. This condition, first described in the medical literature in the late 1970s, primarily affects the hair on the scalp, but may also impact hair on other parts of the body.
Individuals with Steely Hair Syndrome often present with hair that is stiff, dry, coarse, and straw-like in appearance. The hairs appear unruly and cannot be easily combed or flattened. They develop a characteristic tousled or uncombed appearance, hence the alternative name for the syndrome. The hair strands are usually light in color, such as blond or silver, but in some cases can be darker shades.
The cause of Steely Hair Syndrome is linked to mutations in certain genes responsible for hair growth and structure. These mutations affect the shape and texture of the hair follicles, leading to the abnormally shaped hairs. In most cases, the syndrome is inherited in an autosomal dominant pattern, meaning that an affected individual has a 50% chance of passing on the genetic mutation to their offspring.
Although Steely Hair Syndrome is a benign condition and does not cause any significant health issues, individuals with this disorder may experience some psychological and social challenges due to the distinct appearance of their hair. Additionally, the hair may be more vulnerable to damage and breakage.
Currently, there is no specific treatment for Steely Hair Syndrome. However, proper hair care techniques, including gentle brushing, moisturizing products, and avoiding excessive heat or chemical treatments, can help manage the hair's appearance and minimize potential damage.
