Double Outlet Right Ventricle (DORV) is a congenital heart defect characterized by the abnormal positioning of the major blood vessels exiting the heart. In a normal heart, the aorta arises from the left ventricle, while the pulmonary artery arises from the right ventricle. However, in DORV, both the aorta and the pulmonary artery are connected to the right ventricle, which can lead to functional issues and impaired blood flow.
In DORV, the abnormal positioning of the blood vessels often results in a ventricular septal defect (VSD), a hole in the wall that separates the two lower chambers of the heart. This allows oxygenated and deoxygenated blood to mix, reducing the amount of oxygenated blood that reaches the body. The severity of the defect varies, depending on the size of the VSD and the degree of obstruction in the outflow of blood.
This condition is usually present at birth and may cause symptoms such as bluish skin due to inadequate oxygenation, breathing difficulties, poor feeding, and lack of growth. Diagnosis is typically confirmed through various imaging techniques such as echocardiography, magnetic resonance imaging (MRI), or cardiac catheterization.
Treatment for DORV usually involves surgical repair to redirect the blood flow into the correct pathways and repair any associated defects, such as closing the VSD. In some cases, multiple surgeries may be necessary as the child grows and develops. Close monitoring and follow-up care are essential to ensure the best possible outcomes for individuals with DORV.
