How Do You Spell CARBAMOYLPHOSPHATE SYNTHETASE I?

Pronunciation: [kˈɑːbɐmˌɔ͡ɪlfəsfˌe͡ɪt sˈɪnθɪtˌe͡ɪs ˈa͡ɪ] (IPA)

Carbamoylphosphate Synthetase I is a complex word that scientists use in the field of biochemistry. The spelling of this word can be confusing, but it can be broken down using IPA phonetic transcription, which is used to represent the sounds of speech. The correct spelling is /kɑːrˌbæˌmoɪlˈfɑːsfetˌeɪs ˈaɪ/. This enzyme plays a critical role in the urea cycle, which is essential for removing ammonia from the body. Understanding the spelling of this word can help researchers communicate about this vital enzyme with accuracy and precision.

CARBAMOYLPHOSPHATE SYNTHETASE I Meaning and Definition

1. Carbamoylphosphate synthetase I (CPSI) is an enzyme that plays a critical role in the urea cycle, a metabolic pathway that is responsible for removing toxic ammonia from the body. CPSI is the first enzyme in this cycle and catalyzes the formation of carbamoylphosphate from bicarbonate, ammonia, and two molecules of ATP.

   Carbamoylphosphate is an important intermediate compound that is subsequently used in the urea cycle to produce urea, which is then excreted in the urine. This process occurs primarily in the liver and is essential for maintaining nitrogen balance in the body.

   CPSI is a mitochondrial enzyme, meaning it is located in the mitochondria, the energy-producing organelles within cells. It is a large protein that consists of multiple subunits and has multiple active sites. Its function is tightly regulated to ensure efficient urea synthesis and prevent the accumulation of toxic ammonia.

   Deficiencies in CPSI can lead to a disorder called carbamoylphosphate synthetase I deficiency, which is a rare genetic disorder characterized by impaired urea synthesis. This can result in the buildup of ammonia in the body, leading to hyperammonemia, a condition that can be life-threatening if not properly managed. Treatment for CPSI deficiency often involves dietary modifications, medications, and other supportive measures to lower ammonia levels and prevent complications.

Common Misspellings for CARBAMOYLPHOSPHATE SYNTHETASE I

• xarbamoylphosphate synthetase i
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